Search on: IDIOPATHIC FIBROSING ALVEOLITIS, CHRONIC FORM 
Descriptors Found: 1
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Descriptor English:   Idiopathic Pulmonary Fibrosis 
Descriptor Spanish:   Fibrosis Pulmonar Idiopática 
Descriptor Portuguese:   Fibrose Pulmonar Idiopática 
Synonyms English:   Familial Idiopathic Pulmonary Fibrosis
Fibrocystic Pulmonary Dysplasia
Fibrosing Alveolitis, Cryptogenic
Hamman-Rich Disease
Idiopathic Fibrosing Alveolitis, Chronic Form
Idiopathic Pulmonary Fibrosis, Familial
Interstitial Pneumonitis, Usual
Pulmonary Fibrosis, Idiopathic
Usual Interstitial Pneumonia
Cryptogenic Fibrosing Alveolitides
Disease, Hamman-Rich
Diseases, Hamman-Rich
Dysplasia, Fibrocystic Pulmonary
Dysplasias, Fibrocystic Pulmonary
Fibrocystic Pulmonary Dysplasias
Fibrosing Alveolitides, Cryptogenic
Hamman Rich Disease
Hamman-Rich Diseases
Idiopathic Pulmonary Fibroses
Interstitial Pneumonia, Usual
Interstitial Pneumonias, Usual
Interstitial Pneumonitides, Usual
Pneumonitides, Usual Interstitial
Pneumonitis, Usual Interstitial
Pulmonary Dysplasia, Fibrocystic
Pulmonary Dysplasias, Fibrocystic
Pulmonary Fibroses, Idiopathic
Usual Interstitial Pneumonias
Usual Interstitial Pneumonitides
Usual Interstitial Pneumonitis
Cryptogenic Fibrosing Alveolitis  
Tree Number:   C08.381.483.487.500
C08.381.765.500
Definition English:   A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change. 
Indexing Annotation English:   do not confuse with PULMONARY FIBROSIS
History Note English:   2009 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   53083 
Unique Identifier:   D054990 

Occurrence in VHL:
 

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